English Translation, Synonyms, Definitions and Usage Examples of Spanish Word ‘enfermedad de Degos’. Meanings of “enfermedad de degos” in English Spanish Dictionary: 1 result(s) Meanings of “enfermedad de degos” with other terms in English Spanish. Me llamo Loli tengo 37 años y vivo en Madrid y me diagnoticaron la enfermedad de Degos en despues de que perdiera la vision del ojo.
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May Pages ee22 Pages The material is in no way intended to replace professional degso care by a qualified specialist and should not be used as a basis for diagnosis or treatment. Hypotheses implicating vasculitis, coagulopathy or a primary dysfunction of endothelial cells have been proposed. Check this box if you wish to receive a copy of your message.
Malignant atrophic papulosis MAP is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim. Idiopathic, monosymptomatic, cutaneous presentations are benign, however, systemic manifestations can develop years after the occurrence of skin lesions.
Later a wedge-shaped connective tissue necrosis in the deep dermis, due to a thrombotic occlusion of the small arteries and sparse lymphocytes, occurs.
Continuing navigation will be considered as acceptance of this use. Etiology The etiopathogenesis of the disease remains unknown.
Therapeutic efforts with anticoagulants and compounds that facilitate blood perfusion, such as acetylosalicylic acid, pentoxifylline, dipyridamole, ticlodipine and heparin have achieved a partial regression of skin lesions in some individual cases.
Management and treatment Therapeutic efforts with anticoagulants and compounds that facilitate blood perfusion, such as acetylosalicylic acid, pentoxifylline, dipyridamole, ticlodipine and heparin have achieved a partial regression of skin lesions in some individual cases.
Enfermedad de Degos
The documents contained in this web site are presented for information purposes only. More developed lesions can imitate lichen sclerosus see this term.
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Orphanet: Enfermedad de Degos
SRJ is a prestige metric based on the idea that not all citations are the same. Are you a health professional able to prescribe or dispense drugs? Ocular involvement, which affects the eyelids, conjuctiva, retina, sclera and the choroid plexus, as well as the development of diplopia and ophthalmoplegia as secondary side effects of the neurologic involvementhas also been described. To improve our services and products, we use “cookies” own or third parties authorized to show advertising related to client preferences through the analyses of navigation customer behavior.
Health care resources for this disease Expert centres 69 Diagnostic tests 0 Patient organisations 21 Orphan drug s 0. Systemic manifestations are progressive and may lead to serious complications: Only comments written in English can be processed. The histology of early lesions resembles cutaneous lupus erythematosus see this term.
Degos disease – Wikidata
Subscriber If you already have your login data, please click here. A clinical inspection of the skin should be combined with additional examinations including brain magnetic resonance tomography, gastroscopy, colonoscopy, X-ray of the chest and abdominal ultrasound, in order to assess the long-term prognosis. This enferrmedad has received. Summary Epidemiology Less than cases have been described in the literature.
enfermedad de degos
No effective treatment for the systemic manifestations has been established, however, subcutaneous treprostinil has been tested successfully in one case with intestinal and CNS manifestations. Read this article in English. Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted. As all patients may potentially develop the systemic, life-threatening variant, enfermdead annual follow-up is mandatory.
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For all other comments, please send your remarks via contact us. More developed lesions show prominent changes in the dermoepidermal junction, with atrophy of the epidermis and an area of sclerosis in the papillary dermis. Genetic counseling A genetic predisposition with an autosomal dominant trait has been suggested.
Subscribe to our Newsletter. Go to the members area of the website of the AEDV, https: Face, scalp, palms of hands and soles of feet are rarely involved.
Clinical description MAP onset occurs in adults aged with skin lesions that appear initially as small erythematous papules, predominantly on the trunk and the upper extremities. Summary and related texts. CiteScore measures enferrmedad citations received per document published.
Disease definition Malignant atrophic papulosis MAP is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central entermedad atrophy and a surrounding teleangiectatic rim.
It may more rarely manifest as pericarditis or in other organs such as the lungs, presenting as pleuritis. Systemic lesions may affect the gastrointestinal tract and the central nervous system CNS and are potentially lethal. The etiopathogenesis of the disease remains unknown. Xegos Idiopathic, monosymptomatic, cutaneous presentations are benign, however, systemic manifestations can develop years after the occurrence of skin lesions.